Deletion of exon 20 of the Familial Dysautonomia gene Ikbkap in mice causes developmental delay, cardiovascular defects, and early embryonic lethality.

Familial Dysautonomia (FD) is an autosomal recessive disorder that affects 1/3,600 live births in the Ashkenazi Jewish population, and leads to death before the age of 40.The disease is characterized by abnormal development and progressive degeneration of the sensory and autonomic nervous system.A single base pair substitution in intron 20 of the I

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Robust porous hydrogen-bonded organic frameworks: Synthesis and applications in gas adsorption and separation

Being an emerging family of crystalline porous materials, hydrogen-bonded organic frameworks (HOFs) are types of ordered supramolecular structures that constructed from organic linkers (including those with organometallic units) via mainly hydrogen bonds.HOFs Covers have now attracted increasing attention in various fields, owing to their valued fe

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The Nearctic-Caribbean species Leptotrachelus dorsalis (Fabricius, 1801): Larval descriptions with a diagnosis of immature Ctenodactylini and natural history notes on the genus and tribe (Coleoptera, Carabidae)

Adults and larvae of Leptotrachelus dorsalis (Fabricius), the Sugarcane Savior Beetle, Makeup live in association with grasses, the larvae in the appressed leaf axils.Both adult and larval L.dorsalis eat larvae of the Sugarcane Borer, Diatraea saccharalis (Fabricius), and perhaps other insects living in the confines of the leaf sheaths of that and

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